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Previous Volume 336:267-276 January 23, 1997 Number 4 Next

	Since this article has no abstract, we have provided an extract of the first 100 words of the full text and any section headings.

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Restrictive cardiomyopathy is defined as heart-muscle disease that results in impaired ventricular filling, with normal or decreased diastolic volume of either or both ventricles. Systolic function usually remains normal, at least early in the disease, and wall thickness may be normal or increased, depending on the underlying cause.¹ The condition usually results from increased stiffness of the myocardium that causes pressure within the ventricle (or ventricles) to rise precipitously with only small increases in volume. Since the condition affects either or both ventricles, it may cause symptoms and signs of right or left ventricular failure. Often, right-sided findings predominate, with . . . [Full Text of this Article]

Pathogenesis, Natural History, and Specific Findings

Idiopathic Restrictive Cardiomyopathy

Amyloidosis

Endomyocardial Fibrosis and Eosinophilic Cardiomyopathy

Other Infiltrative and Storage Diseases

Other Restrictive Conditions

Presentation

Diagnostic Evaluation

Distinction between Restrictive Cardiomyopathy and Constrictive Pericarditis

Treatment

Symptomatic Therapy

Specific Therapy

            Cardiac Amyloidosis

            Endomyocardial Fibrosis and Eosinophilic Cardiomyopathy

Other Conditions

Source Information

From the Cardiovascular Institute, Box 1030, Mount Sinai Medical Center, 1 Gustave Levy Pl., New York, NY 10029, where reprint requests should be addressed to Dr. Kushwaha.

References

Related Letters:

Restrictive Cardiomyopathy
Reisinger J., Dubrey S. W., Falk R. H., Spodick D. H., Kushwaha S. S., Fallon J. T., Fuster V.
Extract | Full Text  
N Engl J Med 1997; 336:1917-1918, Jun 26, 1997. Correspondence

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