To the Editor: Isolated noncompaction of the ventricular myocardiumis a rare congenital disorder. We have reported elsewhere thatthe incidence of this unique cardiomyopathy is 0.05 percentin adults.1 In the report of the 1995 World Health OrganizationInternationalSociety and Federation of Cardiology task force on the definitionand classification of cardiomyopathies, noncompacted myocardiumhas been categorized as unclassified cardiomyopathy.2
Noncompaction refers to the arrest of compaction of the looselyinterwoven meshwork of myocardial fibers during embryogenesis.3The loose meshwork becomes more compact toward the epicardialsurface and condenses to a compact wall, and the intertrabecularrecesses communicating with . . . [Full Text of this Article]
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