FREE NEJM E-TOC    HOME   |   SUBSCRIBE   |   CURRENT ISSUE   |   PAST ISSUES   |   COLLECTIONS   |   Search Term  Advanced Search

Sign in | Get NEJM's E-Mail Table of Contents — Free | Subscribe

Previous Volume 343:366-368 August 3, 2000 Number 5 Next

	Since this article has no abstract, we have provided an extract of the first 100 words of the full text and any section headings.

	Full Text Purchase this article Add to Personal Archive Add to Citation Manager Notify a Friend E-mail When Cited Related Article by Pyeritz, R. E. Related Article by Pepin, M. PubMed Citation

To the Editor: As one of the medical advisers to the Ehlers–Danlos Support Group in Britain, I have examined and advised more than a dozen families with Ehlers–Danlos syndrome type IV. I would like to draw attention to a few clinical features that did not appear to be present in the large series of patients studied by Pepin et al. (March 9 issue).¹ In my experience, teenage boys are at high risk for arterial rupture, which is often fatal. This may be because during the prepubertal growth spurt, the defective collagen is further weakened. In addition, patients who undergo surgery . . . [Full Text of this Article]

References

This article has been cited by other articles:

• Oderich, G. S. (2006). Current Concepts in the Diagnosis and Management of Vascular Ehlers-Danlos Syndrome. PERSPECT VASC SURG ENDOVASC THER 18: 206-214  
• Ng, S. C., Muiesan, P. (2005). Spontaneous liver rupture in Ehlers-Danlos syndrome type IV. JRSM 98: 320-322 [Full Text]  
• (2003). Radiology Quiz Case 2--Diagnosis. Arch Otolaryngol Head Neck Surg 129: 597-597 [Full Text]