Idiopathic pulmonary fibrosis (IPF) is a progressive diseasecharacterized by fibrosis and remodeling of the lung parenchyma.The median survival of patients with the disease is about threeyears after diagnosis or five years after the onset of symptoms.The pathological findings are those of usual interstitial pneumonia.1In many instances, the diagnosis can be made when typical clinicaland radiologic features are present.2,3,4,5 The classic radiologicfeatures are a patchy pattern of peripheral "honeycombing" thatis more prominent in the bases of the lungs, traction bronchiectasis,and the absence of prominent ground-glass opacity. When thesefindings are not present, . . . [Full Text of this Article]
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From the Department of Medicine, University of Iowa and Veterans Affairs Medical Center, Iowa City.
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