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Previous Volume 346:1486-1488 May 9, 2002 Number 19 Next

	Since this article has no abstract, we have provided an extract of the first 100 words of the full text and any section headings.

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Medical students often learn axioms in order to remember the key features of a disorder. The "rule of 10" used to describe pheochromocytomas is a good example: 10 percent are extraadrenal, and of those, 10 percent are extraabdominal; 10 percent are malignant; 10 percent are found in patients who do not have hypertension; and finally, 10 percent are hereditary.¹ Familial pheochromocytoma is inherited as an autosomal dominant trait alone or as a component of the multiple endocrine neoplasia type 2 syndromes (MEN-2A and MEN-2B), von Hippel–Lindau disease, or, in rare cases, neurofibromatosis type 1.² The remaining 90 percent of pheochromocytomas . . . [Full Text of this Article]

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