
View larger version (57K):
|
A 28-year-old woman with tuberous sclerosis presented with sudden onset of dyspnea and discomfort in the right chest and back. On examination she had tachycardia, tachypnea, and hypoxia, with an absence of breath sounds on the right side. An anteroposterior chest radiograph showed a complete pneumothorax (Panel A, arrowheads), which resolved with a tube thoracostomy. Computed tomographic scans of the chest from previous hospitalizations showed a diffuse cystic intrapulmonary disease pattern consistent with pulmonary lymphangioleiomyomatosis (Panel B, arrows). After successful pulmonary re-expansion, the patient was discharged, but she returned within 1 week with bilateral pneumothoraxes. Pleurodesis was successful on the . . . [Full Text of this Article] |